Table 1.

WHO-EORTC classification of cutaneous lymphomas with primary cutaneous manifestations


Cutaneous T-cell and NK-cell lymphomas 
   Mycosis fungoides  
   MF variants and subtypes  
      Folliculotropic MF  
      Pagetoid reticulosis  
      Granulomatous slack skin  
   Sézary syndrome  
   Adult T-cell leukemia/lymphoma  
   Primary cutaneous CD30+ lymphoproliferative disorders  
      Primary cutaneous anaplastic large cell lymphoma  
      Lymphomatoid papulosis  
   Subcutaneous panniculitis-like T-cell lymphoma* 
   Extranodal NK/T-cell lymphoma, nasal type  
   Primary cutaneous peripheral T-cell lymphoma, unspecified  
      Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional)  
      Cutaneous γ/δ T-cell lymphoma (provisional)  
      Primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoma (provisional)  
Cutaneous B-cell lymphomas 
   Primary cutaneous marginal zone B-cell lymphoma  
   Primary cutaneous follicle center lymphoma  
   Primary cutaneous diffuse large B-cell lymphoma, leg type  
   Primary cutaneous diffuse large B-cell lymphoma, other Intravascular large B-cell lymphoma  
Precursor hematologic neoplasm 
   CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma)†
 

Cutaneous T-cell and NK-cell lymphomas 
   Mycosis fungoides  
   MF variants and subtypes  
      Folliculotropic MF  
      Pagetoid reticulosis  
      Granulomatous slack skin  
   Sézary syndrome  
   Adult T-cell leukemia/lymphoma  
   Primary cutaneous CD30+ lymphoproliferative disorders  
      Primary cutaneous anaplastic large cell lymphoma  
      Lymphomatoid papulosis  
   Subcutaneous panniculitis-like T-cell lymphoma* 
   Extranodal NK/T-cell lymphoma, nasal type  
   Primary cutaneous peripheral T-cell lymphoma, unspecified  
      Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional)  
      Cutaneous γ/δ T-cell lymphoma (provisional)  
      Primary cutaneous CD4+ small/medium-sized pleomorphic T-cell lymphoma (provisional)  
Cutaneous B-cell lymphomas 
   Primary cutaneous marginal zone B-cell lymphoma  
   Primary cutaneous follicle center lymphoma  
   Primary cutaneous diffuse large B-cell lymphoma, leg type  
   Primary cutaneous diffuse large B-cell lymphoma, other Intravascular large B-cell lymphoma  
Precursor hematologic neoplasm 
   CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma)†
 
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