Outcome of treatment presented for patients with severe hemophilia and moderate hemophilia
. | 1972 . | 1978 . | 1985 . | 1992 . | 2001 . |
---|---|---|---|---|---|
Severe hemophilia, N | 159 | 245 | 384 | 387 | 420 |
Hemorrhages, median no. per year (range)* | |||||
Children, 0-16 y | 20 (0-98) | 20 (0-70) | 10 (0-65) | 10 (0-98) | 5 (0-51) |
Adolescents, 17-25 y | 20 (0-98) | 17 (0-100) | 10 (0-90) | 10 (0-98) | 6 (0-75) |
Adult, older than 25 y | 14 (0-97) | 15 (0-100) | 10 (0-90) | 10 (0-82) | 7 (0-75) |
Hospital admissions* | |||||
Hemophilia, % | 51 | 38 | 25 | 22 | 22 |
Dutch males, % | — | — | 6 | 6 | 5 |
Duration of stay, median no. of d/patient (range) | 28 (2-252) | 20 (1-180) | 11 (1-100) | 5 (0-330) | 7 (0-89) |
Absenteeism due to hemophilia, d (range)* | |||||
School† | 30 (0-80) | 15 (0-80) | 4 (0-80) | 2,5 (0-80) | 7 (0-90) |
Work‡ | 15 (0-80) | 20 (0-213) | 7 (0-319) | 8 (0-330) | 5 (0-365) |
Moderate hemophilia | 23 | 106 | 175 | 173 | 176 |
Hemorrhages, median no. per year (range)* | |||||
Children, 0-16 y | 4 (0-40) | 10 (0-104) | 3 (0-66) | 7 (33) | 2 (0-57) |
Adult, older than 25 y | 4 (0-50) | 5 (0-100) | 2 (0-40) | 3 (0-52) | 1 (0-71) |
Hospital admissions* | |||||
Admitted, % | 51 | 27 | 23 | 22 | 15 |
Duration of stay, median no. of d/patient (range) | 17 (2-180) | 10 (1-50) | 7 (1-50) | 5 (0-72) | 6 (0-31) |
Absenteeism due to hemophilia, d (range)* | |||||
School† | 30 (0-80) | 5 (0-80) | 3 (0-50) | 0 (0-15) | 5 (0-20) |
Work‡ | 2 (0-80) | 13 (0-130) | 7 (0-319) | 5 (0-365) | 3 (0-120) |
. | 1972 . | 1978 . | 1985 . | 1992 . | 2001 . |
---|---|---|---|---|---|
Severe hemophilia, N | 159 | 245 | 384 | 387 | 420 |
Hemorrhages, median no. per year (range)* | |||||
Children, 0-16 y | 20 (0-98) | 20 (0-70) | 10 (0-65) | 10 (0-98) | 5 (0-51) |
Adolescents, 17-25 y | 20 (0-98) | 17 (0-100) | 10 (0-90) | 10 (0-98) | 6 (0-75) |
Adult, older than 25 y | 14 (0-97) | 15 (0-100) | 10 (0-90) | 10 (0-82) | 7 (0-75) |
Hospital admissions* | |||||
Hemophilia, % | 51 | 38 | 25 | 22 | 22 |
Dutch males, % | — | — | 6 | 6 | 5 |
Duration of stay, median no. of d/patient (range) | 28 (2-252) | 20 (1-180) | 11 (1-100) | 5 (0-330) | 7 (0-89) |
Absenteeism due to hemophilia, d (range)* | |||||
School† | 30 (0-80) | 15 (0-80) | 4 (0-80) | 2,5 (0-80) | 7 (0-90) |
Work‡ | 15 (0-80) | 20 (0-213) | 7 (0-319) | 8 (0-330) | 5 (0-365) |
Moderate hemophilia | 23 | 106 | 175 | 173 | 176 |
Hemorrhages, median no. per year (range)* | |||||
Children, 0-16 y | 4 (0-40) | 10 (0-104) | 3 (0-66) | 7 (33) | 2 (0-57) |
Adult, older than 25 y | 4 (0-50) | 5 (0-100) | 2 (0-40) | 3 (0-52) | 1 (0-71) |
Hospital admissions* | |||||
Admitted, % | 51 | 27 | 23 | 22 | 15 |
Duration of stay, median no. of d/patient (range) | 17 (2-180) | 10 (1-50) | 7 (1-50) | 5 (0-72) | 6 (0-31) |
Absenteeism due to hemophilia, d (range)* | |||||
School† | 30 (0-80) | 5 (0-80) | 3 (0-50) | 0 (0-15) | 5 (0-20) |
Work‡ | 2 (0-80) | 13 (0-130) | 7 (0-319) | 5 (0-365) | 3 (0-120) |