Table 1. Clinical data of DALD patients... | American Society of Hematology

Table 1.

Clinical data of DALD patients

Patient no.	Sex	Age, y*	IgG, mg/dL†	OPN, ng/mL†	OPN genotype	ANA	AM	HM	SM	Autoimmunities
1	M	6	966	332	AB	+	+	+	+	AHA, AN, T, RF
2	M	10	1100	254	AA	-	+	-	+	AN, E
3	M	16	506	ND	CC	-	+	-	+	AN, T
4	M	9	1143	286	AC	+	-	-	+	AHA, A
5	F	18	2775	426	AB	+	-	-	+	AN, RF
6	M	16	2810	405	CC	-	+	-	+	T, IH
7	F	24	1259	337	AC	+	-	+	+	AHA, IH
8	F	15	1019	222	AC	+	-	-	+	AHA, T, A1
9	M	16	1132	340	AB	+	-	+	+	AHA, T, IH
10	M	11	679	90	AA	+	+	+	+	AHA, T, V
11	F	11	1542	347	AB	+	+	-	+	AHA,
12	F	17	836	211	AC	+/-	-	-	+	AHA, T, E
13	M	15	1153	298	AC	-	+	-	-	T
14	M	5	900	156	AC	+	+	-	+	T
15	M	10	1117	226	AC	+	+	+	+	AN, T, IH
16	M	33	984	494	BC	ND	+	+	+	AN, T, A1
17	M	6	878	109	CC	+	+	-	-	T
18	F	7	1180	167	AA	+	+	+	+	AHA, AN, T, E, A, C, SR, RF
19	M	10	830	103	AC	+	+	-	+	IDDM, T, A1, AN
20	M	6	ND	37	AC	+	+	-	+	AN, T
21	M	13	ND	383	AC	-	+	-	+	AN
22	F	3	ND	187	AB	+	+	+	+	SR
23	M	17	2110	356	AC	+	+	+	+	AHA, AN, T, RF
24	F	9	842	147	AC	+	-	-	+	T
25	M	2	ND	512	AC	+	+	-	+	AHA, IH, T
26	M	11	ND	365	AB	ND	+	+	+	AN, T

Patient no.	Sex	Age, y*	IgG, mg/dL†	OPN, ng/mL†	OPN genotype	ANA	AM	HM	SM	Autoimmunities
1	M	6	966	332	AB	+	+	+	+	AHA, AN, T, RF
2	M	10	1100	254	AA	-	+	-	+	AN, E
3	M	16	506	ND	CC	-	+	-	+	AN, T
4	M	9	1143	286	AC	+	-	-	+	AHA, A
5	F	18	2775	426	AB	+	-	-	+	AN, RF
6	M	16	2810	405	CC	-	+	-	+	T, IH
7	F	24	1259	337	AC	+	-	+	+	AHA, IH
8	F	15	1019	222	AC	+	-	-	+	AHA, T, A1
9	M	16	1132	340	AB	+	-	+	+	AHA, T, IH
10	M	11	679	90	AA	+	+	+	+	AHA, T, V
11	F	11	1542	347	AB	+	+	-	+	AHA,
12	F	17	836	211	AC	+/-	-	-	+	AHA, T, E
13	M	15	1153	298	AC	-	+	-	-	T
14	M	5	900	156	AC	+	+	-	+	T
15	M	10	1117	226	AC	+	+	+	+	AN, T, IH
16	M	33	984	494	BC	ND	+	+	+	AN, T, A1
17	M	6	878	109	CC	+	+	-	-	T
18	F	7	1180	167	AA	+	+	+	+	AHA, AN, T, E, A, C, SR, RF
19	M	10	830	103	AC	+	+	-	+	IDDM, T, A1, AN
20	M	6	ND	37	AC	+	+	-	+	AN, T
21	M	13	ND	383	AC	-	+	-	+	AN
22	F	3	ND	187	AB	+	+	+	+	SR
23	M	17	2110	356	AC	+	+	+	+	AHA, AN, T, RF
24	F	9	842	147	AC	+	-	-	+	T
25	M	2	ND	512	AC	+	+	-	+	AHA, IH, T
26	M	11	ND	365	AB	ND	+	+	+	AN, T

ANA indicates antinuclear antibodies; AM, adenomegaly; HM, hepatomegaly; SM, splenomegaly; +, presence; -, absence; AHA, autoimmune hemolytic anemia; AN, autoimmune neutropenia; T, thrombocytopenia; RF, recurrent fever; E, eczema; ND, not determined; A, arthritis; IH, immune hepatitis; AI, alopecia; V, vitiligo; C, celiac disease; SR, skin rush; and IDDM, insulin-dependent diabetes mellitus.

Age at study.

†

Serum levels; 95th percentile of control OPN levels = 298 ng/mL.

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