Hematologic parameters in humans with HS
ID number (age) . | Hemoglobin, g/L . | MCHC, g/dL . | Reticulocytes, % . | Splenectomy, yes/no . |
---|---|---|---|---|
HS1 (8 y) | 104 | 34.4 | 10.7 | No |
HS2 (10 y) | 99 | 36.2 | 15.9 | No |
HS3 (11 y) | 131 | 35.8 | 4.3 | No |
HS4 (4 y) | 131 | 35.8 | 14.5 | No |
HS5 (adult) | 169 | 37.0 | 3.3 | Yes |
HS6 (5 y) | 124 | 34.6 | 4.1 | No |
HS7 (2 y) | 90 | 36.3 | 12.7 | No |
HS8 (4 y) | 88 | 36.4 | 18.1 | No |
HA (16 y) | 55 | 33.5 | 21.1 | Yes |
Normal | 115-150 | 32.0-36.0 | <2.2 | NA |
ID number (age) . | Hemoglobin, g/L . | MCHC, g/dL . | Reticulocytes, % . | Splenectomy, yes/no . |
---|---|---|---|---|
HS1 (8 y) | 104 | 34.4 | 10.7 | No |
HS2 (10 y) | 99 | 36.2 | 15.9 | No |
HS3 (11 y) | 131 | 35.8 | 4.3 | No |
HS4 (4 y) | 131 | 35.8 | 14.5 | No |
HS5 (adult) | 169 | 37.0 | 3.3 | Yes |
HS6 (5 y) | 124 | 34.6 | 4.1 | No |
HS7 (2 y) | 90 | 36.3 | 12.7 | No |
HS8 (4 y) | 88 | 36.4 | 18.1 | No |
HA (16 y) | 55 | 33.5 | 21.1 | Yes |
Normal | 115-150 | 32.0-36.0 | <2.2 | NA |
HS3 and HS4 are half-siblings. HS5 and HS6 are father and daughter. HS7 and HS8 are siblings. HA has a nonspherocytic hemolytic anemia of unknown etiology.
MCHC indicates mean corpuscular hemoglobin concentration; ND, not done; and NA, not applicable.