Table 1.

Clinical characteristics of patient population


Patient no.

Age, y

Major clinical manifestations

Prior therapy
1   37   Mucosal ulcerations, dermatitis anemia, thrombocytopenia, splenomegaly   Prednisone, hydroxyurea, IFN-α, anti-IL-5 antibody (SCH55700)  
2   51   Mucosal ulcerations, dermatitis, splenomegaly   Prednisone, hydroxyurea, IFN-α, anti-IL-5 antibody (SCH55700)  
3   47   Pulmonary fibrosis, dermatitis, splenomegaly   None  
4   36   Splenomegaly   Hydroxyurea  
5   47   Endomyocardial fibrosis, pulmonary fibrosis, dermatitis, splenomegaly   Prednisone, hydroxyurea, IFN-α, cyclosporin A  
6   29   Endomyocardial fibrosis, peripheral neuropathy, splenomegaly   Prednisone, hydroxyurea  
7   33   Endomyocardial fibrosis, hepatosplenomegaly   Imatinib mesylate (100 mg daily)  
8
 
30
 
Myocarditis, sinusitis, obstructive pulmonary disease, splenomegaly
 
Prednisone, hydroxyurea
 

Patient no.

Age, y

Major clinical manifestations

Prior therapy
1   37   Mucosal ulcerations, dermatitis anemia, thrombocytopenia, splenomegaly   Prednisone, hydroxyurea, IFN-α, anti-IL-5 antibody (SCH55700)  
2   51   Mucosal ulcerations, dermatitis, splenomegaly   Prednisone, hydroxyurea, IFN-α, anti-IL-5 antibody (SCH55700)  
3   47   Pulmonary fibrosis, dermatitis, splenomegaly   None  
4   36   Splenomegaly   Hydroxyurea  
5   47   Endomyocardial fibrosis, pulmonary fibrosis, dermatitis, splenomegaly   Prednisone, hydroxyurea, IFN-α, cyclosporin A  
6   29   Endomyocardial fibrosis, peripheral neuropathy, splenomegaly   Prednisone, hydroxyurea  
7   33   Endomyocardial fibrosis, hepatosplenomegaly   Imatinib mesylate (100 mg daily)  
8
 
30
 
Myocarditis, sinusitis, obstructive pulmonary disease, splenomegaly
 
Prednisone, hydroxyurea
 

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