Table 1.

Characteristics of patients

Patient no.Gene analysisInhibiter titer (BU/mL)Allergic reactions
PeakPresent study
Arg248Stop 64 44 No 
Gene deletion exon4-exon8 > 100 26-40 Yes  
Not determined 170 100 No  
Leu57Stop 140 42 No 
Complete gene deletion 19 No 
Asp152Stop > 100 26 Unknown  
Not determined 103 17 Yes (lethal)  
Complete gene deletion 130 12 Yes 
Patient no.Gene analysisInhibiter titer (BU/mL)Allergic reactions
PeakPresent study
Arg248Stop 64 44 No 
Gene deletion exon4-exon8 > 100 26-40 Yes  
Not determined 170 100 No  
Leu57Stop 140 42 No 
Complete gene deletion 19 No 
Asp152Stop > 100 26 Unknown  
Not determined 103 17 Yes (lethal)  
Complete gene deletion 130 12 Yes 
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