Characteristics of patients
Patient no. . | Gene analysis . | Inhibiter titer (BU/mL) . | Allergic reactions . | |
---|---|---|---|---|
Peak . | Present study . | |||
1 | Arg248Stop | 64 | 44 | No |
2 | Gene deletion exon4-exon8 | > 100 | 26-40 | Yes |
3 | Not determined | 170 | 100 | No |
4 | Leu57Stop | 140 | 42 | No |
5 | Complete gene deletion | 19 | 7 | No |
6 | Asp152Stop | > 100 | 26 | Unknown |
7 | Not determined | 103 | 17 | Yes (lethal) |
8 | Complete gene deletion | 130 | 12 | Yes |
Patient no. . | Gene analysis . | Inhibiter titer (BU/mL) . | Allergic reactions . | |
---|---|---|---|---|
Peak . | Present study . | |||
1 | Arg248Stop | 64 | 44 | No |
2 | Gene deletion exon4-exon8 | > 100 | 26-40 | Yes |
3 | Not determined | 170 | 100 | No |
4 | Leu57Stop | 140 | 42 | No |
5 | Complete gene deletion | 19 | 7 | No |
6 | Asp152Stop | > 100 | 26 | Unknown |
7 | Not determined | 103 | 17 | Yes (lethal) |
8 | Complete gene deletion | 130 | 12 | Yes |