Hemostatic variables in individuals with β2-glycoprotein I deficiency
Variable . | Normal range . | Person 1 . | Person 2 . |
---|---|---|---|
PT-INR, ratio | 0.85 -1.25 | 0.86 | 0.89 |
APTT, s | 24.0 -32.6 | 32.3 | ND |
Fibrinogen, mg/dL | 200 -400 | 388 | 259 |
ATIII, % | 80 -130 | 106 | 95 |
Protein C, % | 67 -127 | 137 | 142 |
Free protein S, % | 65 -135 | 135 | 129 |
Total protein S, μg/mL | 4.0 -13.8 | 13.8 | 10.9 |
Plasminogen, % | 80 -130 | 125 | 97 |
α2PI, % | 80 -130 | 115 | 88 |
TAT, ng/mL | <3.5 | 1.0 | 1.2 |
F1+2, nmol/L | 0.20 -1.04 | 0.73 | 0.71 |
PIC, μg/mL | <0.8 | 0.6 | 0.3 |
D-dimer, μg/mL | <1.0 | 0.32 | 0.27 |
Variable . | Normal range . | Person 1 . | Person 2 . |
---|---|---|---|
PT-INR, ratio | 0.85 -1.25 | 0.86 | 0.89 |
APTT, s | 24.0 -32.6 | 32.3 | ND |
Fibrinogen, mg/dL | 200 -400 | 388 | 259 |
ATIII, % | 80 -130 | 106 | 95 |
Protein C, % | 67 -127 | 137 | 142 |
Free protein S, % | 65 -135 | 135 | 129 |
Total protein S, μg/mL | 4.0 -13.8 | 13.8 | 10.9 |
Plasminogen, % | 80 -130 | 125 | 97 |
α2PI, % | 80 -130 | 115 | 88 |
TAT, ng/mL | <3.5 | 1.0 | 1.2 |
F1+2, nmol/L | 0.20 -1.04 | 0.73 | 0.71 |
PIC, μg/mL | <0.8 | 0.6 | 0.3 |
D-dimer, μg/mL | <1.0 | 0.32 | 0.27 |
INR indicates international normalized ratio; ND, not done.