Table 1.

Effect of Enzyme Therapy in Case 2

Enzyme TherapyLiver VolumePlatelets
Splenic Volume
Hemoglobin
(mo)(mL/fold normal)(g%)(μL)
30 U/kg every 2 wk 
1,749/1.2× 1,620/14× 11.3 75,000 
1,655/1.0× 1,056/8× 12.6 92,000 
13 1,623/1.0× 1,004/7× 13.6 99,000 
21 1,758/1.2× 1,230/9× 12.7 75,000 Stop enzyme therapy 
25-29 60 U/kg every wk 
29 1,590/1.0× 1,372/10× 12.2 79,000 
32 1,766/1.2× 905/6.5× 12.7 103,000 
Enzyme TherapyLiver VolumePlatelets
Splenic Volume
Hemoglobin
(mo)(mL/fold normal)(g%)(μL)
30 U/kg every 2 wk 
1,749/1.2× 1,620/14× 11.3 75,000 
1,655/1.0× 1,056/8× 12.6 92,000 
13 1,623/1.0× 1,004/7× 13.6 99,000 
21 1,758/1.2× 1,230/9× 12.7 75,000 Stop enzyme therapy 
25-29 60 U/kg every wk 
29 1,590/1.0× 1,372/10× 12.2 79,000 
32 1,766/1.2× 905/6.5× 12.7 103,000 

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