Effect of Enzyme Therapy in Case 2
Enzyme Therapy . | Liver Volume . | Platelets . | ||
---|---|---|---|---|
. | Splenic Volume . | . | ||
. | Hemoglobin . | . | ||
(mo) . | (mL/fold normal) . | (g%) . | (μL) . | |
. | . | . | . | . |
30 U/kg every 2 wk | ||||
0 | 1,749/1.2× | 1,620/14× | 11.3 | 75,000 |
7 | 1,655/1.0× | 1,056/8× | 12.6 | 92,000 |
13 | 1,623/1.0× | 1,004/7× | 13.6 | 99,000 |
21 | 1,758/1.2× | 1,230/9× | 12.7 | 75,000 Stop enzyme therapy |
25-29 60 U/kg every wk | ||||
29 | 1,590/1.0× | 1,372/10× | 12.2 | 79,000 |
32 | 1,766/1.2× | 905/6.5× | 12.7 | 103,000 |
Enzyme Therapy . | Liver Volume . | Platelets . | ||
---|---|---|---|---|
. | Splenic Volume . | . | ||
. | Hemoglobin . | . | ||
(mo) . | (mL/fold normal) . | (g%) . | (μL) . | |
. | . | . | . | . |
30 U/kg every 2 wk | ||||
0 | 1,749/1.2× | 1,620/14× | 11.3 | 75,000 |
7 | 1,655/1.0× | 1,056/8× | 12.6 | 92,000 |
13 | 1,623/1.0× | 1,004/7× | 13.6 | 99,000 |
21 | 1,758/1.2× | 1,230/9× | 12.7 | 75,000 Stop enzyme therapy |
25-29 60 U/kg every wk | ||||
29 | 1,590/1.0× | 1,372/10× | 12.2 | 79,000 |
32 | 1,766/1.2× | 905/6.5× | 12.7 | 103,000 |