WHO-EORTC classification of cutaneous lymphomas with primary cutaneous manifestations1
Classification . |
---|
Cutaneous T-cell and NK-cell lymphomas |
MF |
MF variants and subtypes |
Folliculotropic MF |
Pagetoid reticulosis |
Granulomatous slack skin |
Sézary syndrome |
Adult T-cell leukemia/lymphoma |
Primary cutaneous CD30+ lymphoproliferative disorders |
Primary cutaneous anaplastic large cell lymphoma |
Lymphomatoid papulosis |
Subcutaneous panniculitis-like T-cell lymphoma |
Extranodal NK-/T-cell lymphoma, nasal type |
Primary cutaneous peripheral T-cell lymphoma, unspecified |
Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional) |
Cutaneous γ/δ T-cell lymphoma (provisional) |
Primary cutaneous CD4+ small-/medium-sized pleomorphic T-cell lymphoma (provisional) |
Cutaneous B-cell lymphomas |
Primary cutaneous marginal zone B-cell lymphoma |
Primary cutaneous follicle center lymphoma |
Primary cutaneous diffuse large B-cell lymphoma, leg type |
Primary cutaneous diffuse large B-cell lymphoma, other intravascular large B-cell lymphoma |
Precursor hematologic neoplasm |
CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma) |
Classification . |
---|
Cutaneous T-cell and NK-cell lymphomas |
MF |
MF variants and subtypes |
Folliculotropic MF |
Pagetoid reticulosis |
Granulomatous slack skin |
Sézary syndrome |
Adult T-cell leukemia/lymphoma |
Primary cutaneous CD30+ lymphoproliferative disorders |
Primary cutaneous anaplastic large cell lymphoma |
Lymphomatoid papulosis |
Subcutaneous panniculitis-like T-cell lymphoma |
Extranodal NK-/T-cell lymphoma, nasal type |
Primary cutaneous peripheral T-cell lymphoma, unspecified |
Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional) |
Cutaneous γ/δ T-cell lymphoma (provisional) |
Primary cutaneous CD4+ small-/medium-sized pleomorphic T-cell lymphoma (provisional) |
Cutaneous B-cell lymphomas |
Primary cutaneous marginal zone B-cell lymphoma |
Primary cutaneous follicle center lymphoma |
Primary cutaneous diffuse large B-cell lymphoma, leg type |
Primary cutaneous diffuse large B-cell lymphoma, other intravascular large B-cell lymphoma |
Precursor hematologic neoplasm |
CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma) |