Table 1

WHO-EORTC classification of cutaneous lymphomas with primary cutaneous manifestations

Classification
Cutaneous T-cell and NK-cell lymphomas 
    MF 
    MF variants and subtypes 
        Folliculotropic MF 
        Pagetoid reticulosis 
        Granulomatous slack skin 
    Sézary syndrome 
    Adult T-cell leukemia/lymphoma 
    Primary cutaneous CD30+ lymphoproliferative disorders 
        Primary cutaneous anaplastic large cell lymphoma 
        Lymphomatoid papulosis 
    Subcutaneous panniculitis-like T-cell lymphoma 
    Extranodal NK-/T-cell lymphoma, nasal type 
    Primary cutaneous peripheral T-cell lymphoma, unspecified 
        Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional) 
        Cutaneous γ/δ T-cell lymphoma (provisional) 
        Primary cutaneous CD4+ small-/medium-sized pleomorphic T-cell lymphoma (provisional) 
Cutaneous B-cell lymphomas 
    Primary cutaneous marginal zone B-cell lymphoma 
    Primary cutaneous follicle center lymphoma 
    Primary cutaneous diffuse large B-cell lymphoma, leg type 
    Primary cutaneous diffuse large B-cell lymphoma, other intravascular large B-cell lymphoma 
Precursor hematologic neoplasm 
    CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma) 
Classification
Cutaneous T-cell and NK-cell lymphomas 
    MF 
    MF variants and subtypes 
        Folliculotropic MF 
        Pagetoid reticulosis 
        Granulomatous slack skin 
    Sézary syndrome 
    Adult T-cell leukemia/lymphoma 
    Primary cutaneous CD30+ lymphoproliferative disorders 
        Primary cutaneous anaplastic large cell lymphoma 
        Lymphomatoid papulosis 
    Subcutaneous panniculitis-like T-cell lymphoma 
    Extranodal NK-/T-cell lymphoma, nasal type 
    Primary cutaneous peripheral T-cell lymphoma, unspecified 
        Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma (provisional) 
        Cutaneous γ/δ T-cell lymphoma (provisional) 
        Primary cutaneous CD4+ small-/medium-sized pleomorphic T-cell lymphoma (provisional) 
Cutaneous B-cell lymphomas 
    Primary cutaneous marginal zone B-cell lymphoma 
    Primary cutaneous follicle center lymphoma 
    Primary cutaneous diffuse large B-cell lymphoma, leg type 
    Primary cutaneous diffuse large B-cell lymphoma, other intravascular large B-cell lymphoma 
Precursor hematologic neoplasm 
    CD4+/CD56+ hematodermic neoplasm (blastic NK-cell lymphoma) 

or Create an Account

Close Modal
Close Modal