Studies on patients with transformed CTCL (MF/SS syndrome)
. | MF patients with LCT . | LCT at first diagnosis MF (%) . | Stage at time LCT (%) . | Median survival, mo . | ||
---|---|---|---|---|---|---|
IA-IIA . | IIB . | IV . | ||||
Dmitrovsky et al8 | 12 | 0/12 (0) | 1/12 (8) | 11/12 (92) | 2 | |
Salhany et al4 | 17 | 7/17 (41) | 6/17 (35) | 11/17 (65) | 12 | |
Greer et al3 | 22 | 9/22 (41) | 9/22 (41) | 13/22 (59) | 12 | |
Diamandidou et al7 | 26 | 9/26 (35) | 7/26 (27) | 10/26 (38) | 7/26 (27) | 19 |
Vergier et al9 * | 45 | 8/45 (18) | 2/45 (4) | 24/45 (53) | 20/45 (44) | 36 |
Barberio et al6 * | 17 | 2/17 (12) | 7/17 (41) | 7/17 (41) | 3/17 (18) | 27 |
Arulogun et al5 | 22 | 7/22 (32) | 3/22 (14) | 11/22 (50) | 7/22 (32) | 27 |
Agar et al1 | 70 | 70/70 (100) | NR | NR | NR | 100 |
This study* | 100 | 42/100 (42) | 10 (10) | 65 (65) | 25 (25) | 24 |
. | MF patients with LCT . | LCT at first diagnosis MF (%) . | Stage at time LCT (%) . | Median survival, mo . | ||
---|---|---|---|---|---|---|
IA-IIA . | IIB . | IV . | ||||
Dmitrovsky et al8 | 12 | 0/12 (0) | 1/12 (8) | 11/12 (92) | 2 | |
Salhany et al4 | 17 | 7/17 (41) | 6/17 (35) | 11/17 (65) | 12 | |
Greer et al3 | 22 | 9/22 (41) | 9/22 (41) | 13/22 (59) | 12 | |
Diamandidou et al7 | 26 | 9/26 (35) | 7/26 (27) | 10/26 (38) | 7/26 (27) | 19 |
Vergier et al9 * | 45 | 8/45 (18) | 2/45 (4) | 24/45 (53) | 20/45 (44) | 36 |
Barberio et al6 * | 17 | 2/17 (12) | 7/17 (41) | 7/17 (41) | 3/17 (18) | 27 |
Arulogun et al5 | 22 | 7/22 (32) | 3/22 (14) | 11/22 (50) | 7/22 (32) | 27 |
Agar et al1 | 70 | 70/70 (100) | NR | NR | NR | 100 |
This study* | 100 | 42/100 (42) | 10 (10) | 65 (65) | 25 (25) | 24 |
MF indicates mycosis fungoides; LCT, large cell transformation; and NR, not reported.
Studies that included only patients with MF.