Presenting symptoms and features of XLP1 patients with associated mortality
. | Incidence . | Mortality . |
---|---|---|
Presenting symptom | ||
HLH | 31.9% | 65.5% |
FIM | 7.7% | 14.3% |
Lymphoma | 14.3% | 7.7% |
Dysgammaglobulinemia | 22% | 5% |
Family history of XLP1 alone | 16.5% | 20% |
Other | 7.7% | 14.3% |
Features occurring at any time | ||
HLH | 35.2% | 65.6% |
FIM | 9.9% | 22.2% |
Lymphoma | 24.2% | 9% |
Dysgammaglobulinemia | 50.5% | 13% |
Other | 15.4% | 28.6% |
. | Incidence . | Mortality . |
---|---|---|
Presenting symptom | ||
HLH | 31.9% | 65.5% |
FIM | 7.7% | 14.3% |
Lymphoma | 14.3% | 7.7% |
Dysgammaglobulinemia | 22% | 5% |
Family history of XLP1 alone | 16.5% | 20% |
Other | 7.7% | 14.3% |
Features occurring at any time | ||
HLH | 35.2% | 65.6% |
FIM | 9.9% | 22.2% |
Lymphoma | 24.2% | 9% |
Dysgammaglobulinemia | 50.5% | 13% |
Other | 15.4% | 28.6% |