Main VWF/ADAMTS13 features of the 3 decedent patients
| Patient no. . | VWFAg, IU/dL . | ADAMTS13Ag, ng/mL . | ADAMTS13 inhibitor titer . | Anti-ADAMTS13 IgG titer* . | Anti-ADAMTS13 IgM titer* . | Anti-ADAMTS13 IgA titer* . |
|---|---|---|---|---|---|---|
| 15 | 350 | < 62.5 | − | 1600 | 0 | > 10 000 |
| 17 | 150 | < 62.5 | +++ | 6400 | 3200 | > 10 000 |
| 22 | 540 | 85 | + | 1600 | 20 | 3 200 |
| Patient no. . | VWFAg, IU/dL . | ADAMTS13Ag, ng/mL . | ADAMTS13 inhibitor titer . | Anti-ADAMTS13 IgG titer* . | Anti-ADAMTS13 IgM titer* . | Anti-ADAMTS13 IgA titer* . |
|---|---|---|---|---|---|---|
| 15 | 350 | < 62.5 | − | 1600 | 0 | > 10 000 |
| 17 | 150 | < 62.5 | +++ | 6400 | 3200 | > 10 000 |
| 22 | 540 | 85 | + | 1600 | 20 | 3 200 |
− indicates negative; +++, high; +, low.
1/dilution.