Table 3.

Common clinical phenotypes of XLP


Phenotype

Frequency, %

Mortality of each phenotype, %
Fulminant IM   58   96  
Lymphoma (mostly extranodal B-cell origin)   30   69  
Hypogammaglobulinemia
 
31
 
45
 

Phenotype

Frequency, %

Mortality of each phenotype, %
Fulminant IM   58   96  
Lymphoma (mostly extranodal B-cell origin)   30   69  
Hypogammaglobulinemia
 
31
 
45
 

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