Table 3.
Common clinical phenotypes of XLP
Phenotype
.
Frequency, %
.
Mortality of each phenotype, %
.
Fulminant IM
58
96
Lymphoma (mostly extranodal B-cell origin)
30
69
Hypogammaglobulinemia
31
45
Phenotype
.
Frequency, %
.
Mortality of each phenotype, %
.
Fulminant IM
58
96
Lymphoma (mostly extranodal B-cell origin)
30
69
Hypogammaglobulinemia
31
45
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