Table 6.

Clinical features at diagnosis according to the primary localization

Extranodal siteOverallElevated
LDH level
Nodal diseaseStage IVB symptomsPoor-risk IPIBone
marrow
Skin 22 
Orbit 13 
Conjunctiva 18 
Salivary glands 46 
Lung 15 1  
Upper airways 12 
Breast 
Thyroid 10 
Urinary tract 
Liver 
Bowel 
Multiple MALT sites 24 11 24 16 
Extranodal siteOverallElevated
LDH level
Nodal diseaseStage IVB symptomsPoor-risk IPIBone
marrow
Skin 22 
Orbit 13 
Conjunctiva 18 
Salivary glands 46 
Lung 15 1  
Upper airways 12 
Breast 
Thyroid 10 
Urinary tract 
Liver 
Bowel 
Multiple MALT sites 24 11 24 16 

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