Table 2. ECD organ involvement in NIH... | American Society of Hematology

Table 2.

ECD organ involvement in NIH patients and in the literature

Organ system and clinical findings	NIH patients,* n (%)	Veyssier-Belot et al† (%)	Haroche et al‡ (%)
Bone	57 (95)	NR	96
Kidney	39 (65)	27	68
Periaortic encasement	37 (62)	NR	66
Hypogonadism	36 (60)	NR	NR
Lung	31 (52)	14	43
Bone pain	28 (47)	47	40
Maxilla and mandible§	24 (47)	NR	NR
Diabetes insipidus	28 (47)	29	25
CNS disease infiltration	23 (38)	17	51
Retro-orbital area ± exophthalmos	15 (27)	29	25
Heart (pseudotumor in RA)	22 (37)	NR	19
Xanthelasma	20 (33)	19	28
Skin	15 (25)	10	NR
Pericardial disease	5 (8)	7	42

Organ system and clinical findings	NIH patients,* n (%)	Veyssier-Belot et al† (%)	Haroche et al‡ (%)
Bone	57 (95)	NR	96
Kidney	39 (65)	27	68
Periaortic encasement	37 (62)	NR	66
Hypogonadism	36 (60)	NR	NR
Lung	31 (52)	14	43
Bone pain	28 (47)	47	40
Maxilla and mandible§	24 (47)	NR	NR
Diabetes insipidus	28 (47)	29	25
CNS disease infiltration	23 (38)	17	51
Retro-orbital area ± exophthalmos	15 (27)	29	25
Heart (pseudotumor in RA)	22 (37)	NR	19
Xanthelasma	20 (33)	19	28
Skin	15 (25)	10	NR
Pericardial disease	5 (8)	7	42

CNS, central nervous system; NR, not reported; RA, right atrioventricular groove.

Number of patients out of the 60 patients prospectively investigated.

Data included 59 cases (1996).³

Data included 122 historical cases (2014).⁴

Panoramic dental imaging was performed in 51 cases.