Table 1.

Clinical and biological characteristics of the studied population

CharacteristicsPatients (n = 130)
Demographic and clinical  
Age, y 45 ± 12 
Male, n (%) 62 (48) 
Body mass index (kg/m224 ± 4 
Systolic blood pressure (mm Hg) 129 ± 17 
Diastolic blood pressure (mm Hg) 75 ± 11 
Heart rate (bpm) 72 ± 13 
Oxygen saturation (%) (n = 105) 95 ± 3 
Referred for, n (%)  
Worsening of dyspnea 56 (41) 
Chest pain 23 (18) 
Palpitations or ECG changes 15 (12) 
Elevation of a cardiac biomarker 7 (5) 
Cardiac imaging abnormalities 9 (7) 
Episode of decompensated heart failure 7 (5) 
Recent stroke 7 (5) 
Pretransplant assessment (kidney/HSCs) 6 (5) 
Cardiovascular risk factors, n (%)  
History of stroke 25 (19) 
Classification of stroke , n = 25  
Cerebral vasculopathy 8 (32) 
Possible ARD-related stroke or undetermined cause 14 (56) 
Other defined cause 3 (12) 
History  
Arterial hypertension 74 (57) 
Diabetes 4 (3) 
Dyslipidemia 1 (1) 
Obesity 8 (6) 
Obstructive sleep apnea syndrome 13 (10) 
Chronic kidney disease  44 (34) 
Active smoking 16 (12) 
Thromboembolic history (PE/DVT) 35 (27) 
Treatment of SCD, n (%)  
None 15 (12) 
Hydroxyurea 81 (62) 
Erythrocytapheresis 10 (8) 
Hydroxyurea + erythrocytapheresis 22 (17) 
Bloodletting 2 (2) 
Anticoagulation therapy and indication, n (%)  
Stroke complicating patient foramen ovale 1 (1) 
Cryptogenic stroke 2 (2) 
History of AF (disregarding complications) 15 (12) 
Venous thromboembolism 14 (11) 
Biology  
Hemoglobin (g/dL) 8.7 ± 1.5 
Leukocytes (×109/L) 7.7 ± 2.6 
Platelets (×109/L) 313 ± 132 
Potassium (mmol/L) 4.3 ± 0.5 
Creatinine (μmol/L) 63 (52-91) 
GFR (based on CKD-EPI formula in mL/min per 1.73m2105 (69-121) 
ASAT (IU/L) 42 (33-60) 
ALAT (IU/L) 24 (18-36) 
LDH (IU/L) 439 (253-494) 
Total bilirubin (μmol/L) 31 (21-47) 
Free bilirubin (μmol/L) 21 (13-33) 
Nt Pro-BNP (ng/L) 145 (57-400) 
Nt Pro-BNP ≥160n g/L 61 (47) 
Troponin T (Hs) (ng/L), n = 101 5 (3-11) 
CharacteristicsPatients (n = 130)
Demographic and clinical  
Age, y 45 ± 12 
Male, n (%) 62 (48) 
Body mass index (kg/m224 ± 4 
Systolic blood pressure (mm Hg) 129 ± 17 
Diastolic blood pressure (mm Hg) 75 ± 11 
Heart rate (bpm) 72 ± 13 
Oxygen saturation (%) (n = 105) 95 ± 3 
Referred for, n (%)  
Worsening of dyspnea 56 (41) 
Chest pain 23 (18) 
Palpitations or ECG changes 15 (12) 
Elevation of a cardiac biomarker 7 (5) 
Cardiac imaging abnormalities 9 (7) 
Episode of decompensated heart failure 7 (5) 
Recent stroke 7 (5) 
Pretransplant assessment (kidney/HSCs) 6 (5) 
Cardiovascular risk factors, n (%)  
History of stroke 25 (19) 
Classification of stroke , n = 25  
Cerebral vasculopathy 8 (32) 
Possible ARD-related stroke or undetermined cause 14 (56) 
Other defined cause 3 (12) 
History  
Arterial hypertension 74 (57) 
Diabetes 4 (3) 
Dyslipidemia 1 (1) 
Obesity 8 (6) 
Obstructive sleep apnea syndrome 13 (10) 
Chronic kidney disease  44 (34) 
Active smoking 16 (12) 
Thromboembolic history (PE/DVT) 35 (27) 
Treatment of SCD, n (%)  
None 15 (12) 
Hydroxyurea 81 (62) 
Erythrocytapheresis 10 (8) 
Hydroxyurea + erythrocytapheresis 22 (17) 
Bloodletting 2 (2) 
Anticoagulation therapy and indication, n (%)  
Stroke complicating patient foramen ovale 1 (1) 
Cryptogenic stroke 2 (2) 
History of AF (disregarding complications) 15 (12) 
Venous thromboembolism 14 (11) 
Biology  
Hemoglobin (g/dL) 8.7 ± 1.5 
Leukocytes (×109/L) 7.7 ± 2.6 
Platelets (×109/L) 313 ± 132 
Potassium (mmol/L) 4.3 ± 0.5 
Creatinine (μmol/L) 63 (52-91) 
GFR (based on CKD-EPI formula in mL/min per 1.73m2105 (69-121) 
ASAT (IU/L) 42 (33-60) 
ALAT (IU/L) 24 (18-36) 
LDH (IU/L) 439 (253-494) 
Total bilirubin (μmol/L) 31 (21-47) 
Free bilirubin (μmol/L) 21 (13-33) 
Nt Pro-BNP (ng/L) 145 (57-400) 
Nt Pro-BNP ≥160n g/L 61 (47) 
Troponin T (Hs) (ng/L), n = 101 5 (3-11) 

The ordinal data are reported as mean ± standard deviation when they have a normal distribution, as median (Q1-Q3) when they do not have a normal distribution, and nominal data as absolute value and percentage.

ALAT, alanine aminotransferase; ASAT, aspartate aminotransferase; bpm, beats per minute; CKD-EPI, Chronic Kidney Disease Epidemiology Collaboration; DVT, deep veinous thrombosis; Hs, high sensitivity; HSCs, hematopoietic stem cells; LDH, lactate dehydrogenase; MRI, magnetic resonance imaging; PE, pulmonary embolism; Q; quartile.

Additional information in supplemental Table 2.

GFR <90 mL/min per 1.73m2 according to CKD-EPI

Close Modal

or Create an Account

Close Modal
Close Modal