Table 1.
Patients with TTP  
Demographics  
Age, y (IQR) 45 (29-53) 
Male, n (%) 12 (40) 
Laboratory features  
Platelets, ×109/L (IQR) 13 (9-30) 
Hemoglobin, g/L (IQR) 73 (60-98) 
LDH, IU/L (IQR) 1348 (871-1715) 
Presence of schistocytes, n (%) 30 (100) 
ADAMTS13 activity, % (IQR) 5 (0-5) 
Anti-ADAMTS13 IgG, IU/mL 71 (51-112) 
Clinical features  
Mortality, n (%) 10 (33) 
Control patients  
Demographics  
Age, y (IQR) 54 (53-58) 
Male, n (%) 5 (50) 
Neurologic disease  
Myasthenia gravis, n (%) 8 (80) 
Acute polyradiculoneuritis, n (%) 2 (20) 
Patients with TTP  
Demographics  
Age, y (IQR) 45 (29-53) 
Male, n (%) 12 (40) 
Laboratory features  
Platelets, ×109/L (IQR) 13 (9-30) 
Hemoglobin, g/L (IQR) 73 (60-98) 
LDH, IU/L (IQR) 1348 (871-1715) 
Presence of schistocytes, n (%) 30 (100) 
ADAMTS13 activity, % (IQR) 5 (0-5) 
Anti-ADAMTS13 IgG, IU/mL 71 (51-112) 
Clinical features  
Mortality, n (%) 10 (33) 
Control patients  
Demographics  
Age, y (IQR) 54 (53-58) 
Male, n (%) 5 (50) 
Neurologic disease  
Myasthenia gravis, n (%) 8 (80) 
Acute polyradiculoneuritis, n (%) 2 (20) 

IgG, immunoglobulin G; IQR, interquartile range; LDH, lactate dehydrogenase.

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