Table 3.

Differences in ADAMTS13 activity, anti-ADAMTS13 IgG antibody, and ADAMTS13 antigen levels between patients who experienced exacerbation and no exacerbation

No exacerbation (n = 61)Exacerbation (n = 4)
Median ADAMTS13 activity (IQR), IU/dL 50 (9.35-80) <10 
Median anti-ADAMTS13 IgG antibody (IQR), % 11 (4-40.5) 80 (33.25-125.3) 
Median ADAMTS13 antigen (IQR), % 63 (37.5-97) 2 (1-3.75) 
No exacerbation (n = 61)Exacerbation (n = 4)
Median ADAMTS13 activity (IQR), IU/dL 50 (9.35-80) <10 
Median anti-ADAMTS13 IgG antibody (IQR), % 11 (4-40.5) 80 (33.25-125.3) 
Median ADAMTS13 antigen (IQR), % 63 (37.5-97) 2 (1-3.75) 

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